The origin of craniofacial structures is a complex embryonary process. There could be different growth alterations of it; one of them is Goltz Syndrome. We report a case of a female patient, 21 years old who present skin, bone and muscular alterations. This alteration is mainly in the left craniofacial structures, resulting in facial asymmetry. She also presented microdontia, enamel hypoplasia, and generalized gingivitis. A severe Temporomandibular disorder (TMD) was also associated with headaches, earaches, dizziness, deafness in the left ear and poor sleep quality. She was treated for 6 months with an occlusal splint, higher in the left side to stimulate the muscular activity and give some relief to the left TMJ tissues. Subsequently, a complete oral rehabilitation treatment was performed to achieve occusal stability and to perpetuate the mandibular position. After the treatment, the patient presented more development in the left muscular and skeletal structures, improving the facial symmetry, and eliminating headaches, earaches, dizziness, deafness in the left ear and poor sleep quality.
KEY WORDS: focal dermal hypoplasia, Goltz syndrome, temporomandibular disorders, facial assimetry.
How to cite this article
OYANGUREN, F. R. & WURGAFT, D. R. Focal dermal hypoplasia or Goltz sindrome. Temporomandibular orthopedic management. Int. J. Odontostomat., 3(1):79-85, 2009.